Microbiology · Year 2 · from Microbiology
Case 2: Invasive Aspergillosis in Neutropenic Patient
Presentation
A 55-year-old man undergoing induction chemotherapy for acute myeloid leukemia has been neutropenic (ANC <100 cells/μL) for 18 days. He has been on broad-spectrum antibiotics for persistent fever without a clear source. He now develops pleuritic chest pain, cough, and hemoptysis. CT chest shows a 3 cm nodule in the right upper lobe surrounded by ground-glass attenuation (halo sign). Serum galactomannan index is elevated at 2.4 (positive >0.5). Bronchoscopy with bronchoalveolar lavage is performed; galactomannan of BAL fluid is markedly elevated.
Clinical Image
CT scan of the chest demonstrating a pulmonary nodule with surrounding ground-glass opacity (halo sign), representing hemorrhage around the invasive fungal focus - characteristic of invasive aspergillosis in neutropenic patients.
Image Source: Lecture image - invasive aspergillosis imaging
Questions
- What is the most likely diagnosis, and what features support this diagnosis?
- Explain the pathophysiology of the halo sign and hemoptysis.
- What is the appropriate treatment, and what determines prognosis?
- What preventive strategies exist for high-risk patients?
Answers
- Diagnosis and supporting features: This is invasive pulmonary aspergillosis (IPA), most likely caused by Aspergillus fumigatus. Supporting features include:
- Prolonged neutropenia (>10 days) - the major risk factor
- Fever unresponsive to broad-spectrum antibiotics
- Characteristic imaging: Pulmonary nodule with halo sign
- Elevated serum galactomannan: A cell wall component detected as a biomarker
- Hemoptysis: Suggests angioinvasion
The combination of host risk factors, clinical presentation, imaging, and biomarker positivity establishes the diagnosis with high probability.
- Pathophysiology of halo sign and hemoptysis: Aspergillus demonstrates angioinvasive behavior in neutropenic patients - the fungal hyphae invade blood vessel walls. This causes:
- Thrombosis of invaded vessels
- Hemorrhage around the infected focus (produces the halo sign = ground-glass surrounding nodule)
- Tissue infarction from vascular occlusion
- Hemoptysis from erosion into airways
- Later, as neutropenia resolves, the air-crescent sign appears as necrotic tissue separates
- Treatment and prognosis:
- First-line therapy: Voriconazole (IV then oral) - superior to amphotericin B
- Alternative: Isavuconazole (similar efficacy, fewer drug interactions, better tolerated)
- Salvage therapy: Liposomal amphotericin B
- Combination therapy: Sometimes used for refractory cases
Prognosis depends on:
- Immune reconstitution - most critical factor; mortality drops significantly when neutropenia resolves
- Early diagnosis and treatment
- Extent of infection
- Underlying disease status
Overall mortality ranges from 30-80% depending on these factors.
- Prevention strategies:
- Antifungal prophylaxis: Posaconazole for high-risk patients (prolonged neutropenia, HSCT with GVHD)
- HEPA-filtered rooms to reduce airborne spore exposure
- Galactomannan monitoring: Twice-weekly testing enables early preemptive therapy
- Avoid high-risk exposures: Construction sites, gardening, areas with decaying vegetation
- Prompt empiric therapy for suspected fungal infection in high-risk neutropenic patients