Neuroscience · Year 2 · from Neuroscience

Case 2: Multiple Sclerosis - Relapsing-Remitting

Patient Presentation

Demographics: 28-year-old female

Chief Complaint: Right eye vision loss and leg weakness

History of Present Illness: The patient developed pain with eye movement in her right eye 5 days ago, followed by progressive vision loss over 3 days. She describes the vision as "looking through wax paper." Her color vision is particularly affected - reds look "washed out." She now recalls that 2 years ago, she had an episode of numbness and tingling in her legs lasting 3 weeks, which she attributed to stress and never sought medical attention for.

Physical Examination:

  • Vital signs: Normal
  • General: Healthy-appearing young woman
  • Neurological:
  • Mental status: Normal
  • Cranial nerves:
  • Visual acuity: Right eye 20/200 (left eye 20/20)
  • Color vision: Cannot identify Ishihara plates with right eye
  • Pupils: Right relative afferent pupillary defect (RAPD) - when light swings to right eye, both pupils dilate (Marcus Gunn pupil)
  • Fundoscopy: Right optic disc slightly swollen (papillitis)
  • Other cranial nerves normal
  • Motor: 5/5 throughout
  • Sensory: Decreased vibration sense at toes bilaterally
  • Reflexes: 3+ throughout; bilateral Babinski signs
  • Coordination: Normal
  • Gait: Normal

Key Findings:

  • Optic neuritis (right)
  • Prior episode of transverse myelitis (history of leg numbness)
  • Signs of prior spinal cord involvement (hyperreflexia, Babinski)
  • = Dissemination in space AND time

Workup:

  • MRI brain with and without contrast: Multiple ovoid T2/FLAIR hyperintense lesions in periventricular white matter oriented perpendicular to the ventricles ("Dawson's fingers"); several juxtacortical lesions; one enhancing lesion (active); one infratentorial lesion
  • MRI spine: Two non-enhancing T2 lesions in cervical cord
  • MRI orbits: Right optic nerve enhancement and swelling
  • Lumbar puncture: Oligoclonal bands present in CSF (absent in serum); elevated IgG index; mild lymphocytic pleocytosis (12 cells)

Diagnosis: Multiple sclerosis, relapsing-remitting (McDonald 2017 criteria satisfied)

Treatment:

Acute Optic Neuritis:

  • IV methylprednisolone 1 gram daily for 3 days
  • Oral prednisone taper over 2 weeks

Disease-Modifying Therapy:

  • Discussed options: moderate efficacy (interferons, glatiramer) vs high efficacy (ocrelizumab, natalizumab)
  • Started ocrelizumab (anti-CD20) given multiple lesions indicating active disease
  • Baseline JCV antibody: Negative
  • Hepatitis B screening: Negative

Other:

  • Vitamin D supplementation (2000 IU daily)
  • Smoking cessation counseling (she is a social smoker)
  • Discussed pregnancy planning (ocrelizumab has washout period)

Clinical Course: Visual acuity improved to 20/30 at 6 weeks; color vision partially recovered. No new relapses occurred on ocrelizumab over 1 year. Surveillance MRI showed no new or enhancing lesions. She remained fully functional, working full-time as an accountant.

Clinical Pearl: Multiple sclerosis diagnosis requires dissemination in space (lesions in multiple CNS locations) and time (new activity over time or simultaneous enhancing and non-enhancing lesions). Optic neuritis is often the presenting manifestation - the triad of painful eye movement, vision loss, and RAPD is classic. Oligoclonal bands in CSF are present in >95% of MS patients. Early treatment with highly effective disease-modifying therapy prevents accumulation of disability. Dawson's fingers (periventricular lesions perpendicular to ventricles) are characteristic of MS and reflect perivenular inflammation.


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