Pathology · Year 2 · from Pathology
Case 2: HIV/AIDS with Opportunistic Infections
Patient Demographics
- Age: 38 years old
- Sex: Male
- Occupation: Graphic designer
Chief Complaint
"Shortness of breath, fever, and white patches in my mouth for 3 weeks"
History of Present Illness
A 38-year-old male presents with progressive shortness of breath and dry cough for 3 weeks. He has had low-grade fevers, drenching night sweats, and has lost 7 kg over the past 2 months. He noticed white patches in his mouth that have become painful. He has had intermittent diarrhea for the past month. He was diagnosed with HIV 5 years ago but stopped taking antiretroviral therapy 2 years ago due to side effects and has not followed up with his HIV provider. He has had multiple male sexual partners.
Physical Examination
- Vital Signs: BP 102/68 mmHg, HR 112 bpm, RR 28/min, Temp 38.6C, SpO2 86% on room air
- General: Cachectic male in moderate respiratory distress
- HEENT: White plaques on oral mucosa and tongue (scrape off), angular cheilitis
- Respiratory: Tachypnea, bilateral crackles throughout, no wheezing
- Lymph nodes: Diffuse lymphadenopathy
- Skin: Seborrheic dermatitis on face, purple nodular lesions on lower extremities
- Neurologic: Alert, no focal deficits
Diagnostic Workup
Laboratory Studies:
| Test | Result | Reference Range |
|---|---|---|
| CD4 count | 45 cells/uL | 500-1500 cells/uL |
| HIV viral load | 450,000 copies/mL | Undetectable on ART |
| WBC | 3,200/uL | 4,500-11,000/uL |
| Hemoglobin | 9.8 g/dL | 13.5-17.5 g/dL |
| LDH | 585 U/L | 140-280 U/L |
| 1,3-beta-D-glucan | 385 pg/mL | <80 pg/mL |
Imaging:
- Chest X-ray: Bilateral diffuse interstitial infiltrates ("ground glass" appearance)
- CT Chest: Bilateral ground-glass opacities with apical sparing, no lymphadenopathy
Bronchoscopy with BAL:
- GMS stain: Cysts with central dot consistent with Pneumocystis jirovecii
- Cytology: No malignant cells
Oral Scraping:
- KOH prep: Budding yeast with pseudohyphae (Candida)
Skin Biopsy (leg lesion):
- Spindle cells forming vascular channels, HHV-8 positive
- Consistent with Kaposi sarcoma
Pathology Correlation
This case demonstrates HIV/AIDS pathology and opportunistic infections:
HIV Pathophysiology:
- HIV targets CD4+ T lymphocytes via CD4 receptor and CCR5/CXCR4 co-receptors
- Progressive CD4 depletion over years
- AIDS defined: CD4 <200 cells/uL OR AIDS-defining illness
Lymph Node Pathology Progression:
- Early: Follicular hyperplasia (robust immune response)
- Late: Follicular involution and lymphocyte depletion (immune exhaustion)
Opportunistic Infections by CD4 Count:
| CD4 Count | Infections |
|---|---|
| <500 | Oral candidiasis, TB, Kaposi sarcoma |
| <200 | PCP, Toxoplasmosis, Cryptococcus |
| <100 | CMV, MAC, Cryptosporidium |
| <50 | Progressive multifocal leukoencephalopathy |
Pneumocystis jirovecii Pneumonia (PCP):
- Most common AIDS-defining illness
- Histology: "Foamy" eosinophilic alveolar exudate
- GMS stain: Cysts with central dot, crushed cup shapes
- Elevated LDH and beta-glucan
- Ground-glass opacities on imaging
Kaposi Sarcoma:
- Caused by HHV-8 (Human herpesvirus 8)
- Histology: Spindle cells forming slit-like vascular spaces, red blood cell extravasation
- Can involve skin, mucosa, lungs, GI tract
Oral Candidiasis (Thrush):
- Pseudomembranous form: White plaques that scrape off
- Histology: Budding yeast with pseudohyphae (not true hyphae)
Clinical Image
Pathology demonstrating pulmonary involvement in AIDS. Pneumocystis jirovecii pneumonia shows characteristic foamy, eosinophilic alveolar exudate. GMS stain reveals the cup-shaped cysts of Pneumocystis.
Image Source: Wikimedia Commons - "Pneumocystis jirovecii" License: CC BY-SA 3.0 URL: https://commons.wikimedia.org/wiki/File:Pneumocystis_jirovecii_01.jpg
Diagnosis
- AIDS (CD4 = 45 cells/uL with AIDS-defining illnesses)
- Pneumocystis jirovecii Pneumonia (PCP)
- Oropharyngeal Candidiasis
- Kaposi Sarcoma
Treatment
PCP:
- TMP-SMX (trimethoprim-sulfamethoxazole) - first line
- Prednisone (if PaO2 <70 or A-a gradient >35)
- Supplemental oxygen
Candidiasis:
- Fluconazole orally
Kaposi Sarcoma:
- Antiretroviral therapy (primary treatment)
- Consider chemotherapy if extensive
HIV:
- Initiate antiretroviral therapy (after treating PCP)
- OI prophylaxis:
- TMP-SMX (PCP, Toxoplasma) until CD4 >200
- Azithromycin (MAC) until CD4 >100
- Adherence counseling
- Partner notification
Teaching Points
- HIV depletes CD4+ T cells, leading to progressive immunodeficiency
- Opportunistic infections occur at predictable CD4 thresholds
- PCP is the most common AIDS-defining illness in the US
- Kaposi sarcoma is caused by HHV-8, an AIDS-defining malignancy
- Type IV hypersensitivity is impaired in HIV, explaining susceptibility to intracellular pathogens
- Effective ART can restore immune function and reduce OI risk