Msk Dermatology · Year 2 · from Msk Dermatology
Case 2: Vitiligo - Melanocyte Destruction
Patient Presentation
Demographics: 28-year-old female
Chief Complaint: Expanding white patches on hands and face
History of Present Illness: The patient noticed depigmented patches on the dorsum of her hands 6 months ago. The patches have slowly expanded and new patches appeared on her face around her eyes and mouth. She has no symptoms (no itching, pain, or scaling). She has a history of hypothyroidism.
Family History:
- Mother has vitiligo
- Aunt has type 1 diabetes
Physical Examination:
- Skin:
- Sharply demarcated, depigmented (chalk-white) macules and patches
- Distribution: Dorsal hands, periorbital, perioral
- Bilateral and symmetric
- No scale, no atrophy
- Wood lamp: Enhanced depigmentation (bright white fluorescence)
- Thyroid: Non-tender, no nodules
Workup and Results
Laboratory Studies:
- TSH: 8.2 mU/L (elevated - known hypothyroidism)
- Anti-TPO antibodies: Positive
Wood Lamp Examination:
- Bright white fluorescence in affected areas
- Helps delineate extent of involvement
Clinical Image
Clinical photograph showing characteristic depigmented patches of vitiligo with sharply demarcated borders, demonstrating the typical distribution around the periorbital and perioral areas.
Diagnosis
Vitiligo (Generalized/Common Type)
Features:
- Acquired depigmentation
- Autoimmune destruction of melanocytes
- Associated autoimmune conditions (thyroid disease)
- Family history of autoimmunity
Discussion
This case illustrates melanocyte biology and destruction:
- Melanocyte Origin: The lecture describes how melanocytes originate from neural crest cells and reside in the stratum basale of the epidermis.
- Autoimmune Destruction: The lecture identifies vitiligo as resulting from autoimmune destruction of melanocytes. T-cell mediated destruction leads to complete loss of melanin production in affected areas.
- Melanin Function: The lecture explains that melanin produced by melanocytes (eumelanin = brown/black; pheomelanin = red/yellow) protects against UV radiation damage. Loss of melanocytes in vitiligo increases photosensitivity.
- Tyrosinase: The lecture notes that tyrosinase is the rate-limiting enzyme in melanin synthesis. Antibodies against melanocyte antigens (including tyrosinase) may contribute to vitiligo pathogenesis.
Treatment Plan
- Sun Protection:
- Sunscreen SPF 30+ (affected areas prone to sunburn)
- Protective clothing
- Topical Therapy:
- Topical corticosteroids (first-line for limited disease)
- Topical calcineurin inhibitors (tacrolimus) - face-safe
- Trial for 3-6 months
- Phototherapy:
- Narrowband UVB for extensive disease
- Stimulates melanocyte migration from hair follicles
- Cosmetic Options:
- Cosmetic camouflage (cover-up makeup)
- Self-tanners (temporary)
- Screening:
- Annual thyroid function tests
- Screen for other autoimmune conditions if symptoms develop
Teaching Points
- Melanocytes originate from neural crest and reside in stratum basale
- Vitiligo results from autoimmune destruction of melanocytes
- Tyrosinase is the rate-limiting enzyme in melanin synthesis
- Vitiligo is associated with other autoimmune conditions (thyroid, diabetes)
- Wood lamp examination enhances depigmented areas